Question: What Is Rasmussen Syndrome?

What is West syndrome?

West syndrome is a constellation of symptoms characterized by epileptic/infantile spasms, abnormal brain wave patterns called hypsarrhythmia and intellectual disability..

What do seizure auras feel like?

For some people with epilepsy, seizures are preceded by a warning. Doctors refer to that warning as an aura, an event that can manifest as music, swirling colors, a memory, a sense of impending doom, a smell or taste, a rising nausea, or an intense sensation of déjà vu.

What causes Rasmussen syndrome?

Recent studies suggest that the cause of Rasmussen’s syndrome is an autoimmune disorder (antibodies are produced against the body’s own tissues) directed against receptors on the brain cells. The process may be triggered by a viral infection, and possibly other triggering causes.

What is Rasmussen syndrome What are its history symptoms prognosis etc )?

Rasmussen Syndrome is associated with progressive neurological issues and seizures in children. Rasmussen’s Syndrome can become present from 14 months old to 14 years old. Symptoms include seizures, mild weakness in the arm or leg, deteriorating thinking/memory (hemiparesis) or language problems (aphasia).

How common is Rasmussen’s encephalitis?

People affected with Rasmussen’s encephalitis may experience permanent brain damage, loss of motor skill and mental deterioration as a result of the chronic inflammation of the brain. The condition is very rare with an estimated 200-500 cases worldwide, and it typically affects children between the ages of 2-10.

What part of the brain does Rasmussen’s syndrome affect?

Other research focuses on finding better wa… Rasmussen’s encephalitis (RE) is a very rare, chronic inflammatory neurological disease that usually affects only one hemisphere (half) of the brain. It most often occurs in children under the age of 10 but can also affect adolescents and adults.

Can Encephalitis be cured?

If a cause of encephalitis is found, treatment will start straight away. Possible treatments include: antiviral medicine – used if encephalitis is caused by the herpes simplex or chickenpox viruses; it’s usually given into a vein three times a day for 2 to 3 weeks.

Why would someone get a hemispherectomy?

A hemispherectomy is a rare surgery where half of the brain is either removed or disconnected from the other half. It’s performed on children and adults who have seizures that don’t respond to medicine.

What things cause seizures?

Causes of seizures can include:Abnormal levels of sodium or glucose in the blood.Brain infection, including meningitis and encephalitis.Brain injury that occurs to the baby during labor or childbirth.Brain problems that occur before birth (congenital brain defects)Brain tumor (rare)Drug abuse.Electric shock.Epilepsy.More items…•Feb 24, 2020

What is Rasmussen syndrome history?

Historical note and terminology The first cases of what is now called Rasmussen encephalitis or Rasmussen syndrome was referred to as chronic focal encephalitis in 1958 by Dr. Theodore Rasmussen and his colleagues at the Montreal Neurological Institute (Rasmussen et al 1958).

Can you remove part of your brain?

Yes, apparently it is, according to a new analysis that assessed brain health among six adults who had undergone a hemispherectomy as children. The highly invasive surgery, which entails removal or severing of half the brain, had been part of a pediatric epilepsy treatment to reduce seizure risk.

What happens in a hemispherectomy?

What Is a Hemispherectomy? A hemispherectomy is when one side of the brain is surgically disconnected from the rest of the brain so that seizures that originate in that hemisphere have nowhere to go. This procedure is also called “functional hemispherectomy.”

What are the most common seizure medications?

Many medications are used in the treatment of epilepsy and seizures, including:Phenytoin (Dilantin, Phenytek)Valproic acid (Depakene)Oxcarbazepine (Oxtellar, Trileptal)Lamotrigine (Lamictal)Gabapentin (Gralise, Neurontin)Topiramate (Topamax)Phenobarbital.Zonisamide (Zonegran)More items…•Feb 24, 2021

Can Lyme Disease cause seizures?

At its worst, neurological Lyme disease can cause paralysis, seizures or schizophrenia. With lesser symptoms, the victim is plagued with insomnia, nightmares, brain fog, word or song iteration, word loss (tip of the tongue) and hypersensitivity to sound, motion, or bright lights.

What are the symptoms of Rasmussen syndrome?

Symptoms of Rasmussen syndrome Rasmussen syndrome typically begins between 1 and 14 years of age. Seizures are often the first symptom to appear. Weakness and other neurological problems, intellectual function (including memory and sometimes, language) often begin 1 to 3 years after the seizures start.

Can you live without half of your brain?

It’s rare but there are few dozens of people who live without large parts of their brain, half or even less. These people weren’t born that way. Most commonly they had a disease in childhood, such as Rasmussen’s encephalitis, where epileptic seizures are very common.

What happens in the brain during a seizure?

During a seizure, there are bursts of electrical activity in your brain, sort of like an electrical storm. This activity causes different symptoms depending on the type of seizure and what part of the brain is involved. Seizures can take on many different forms and affect different people in different ways.

What is the drug Keppra used for?

Levetiracetam is used to treat seizures (epilepsy). It belongs to a class of drugs known as anticonvulsants. Levetiracetam may decrease the number of seizures you have.

Who discovered Rasmussen syndrome?

Rasmussen’s encephalitis was first described by neurosurgeon Theodore Rasmussen and his colleagues in the late 1950s. Since then, the variable clinical features and lack of understanding of cause have created dilemmas in clinical decision making.

Is encephalitis a chronic disease?

Encephalitis is a diffuse inflammatory process of the brain parenchyma associated with evidence of brain dysfunction. The presentation of encephalitis can be acute or chronic.

How is epilepsy diagnosed?

Electroencephalogram (EEG). This is the most common test used to diagnose epilepsy. In this test, electrodes are attached to your scalp with a paste-like substance or cap. The electrodes record the electrical activity of your brain.